en coup de sabre

From French en coup de sabre (literally “by/in a strike of the sword”), so-called because of its resemblance to the scar of a sabre wound.

• (UK) IPA^(key): /ɒn ˌkuː də ˈseɪ.bə(ɹ)/ ~ /ɑ̃ ku də sa.bɹə/

en coup de sabre (not comparable)

1. (medicine) Of a subtype of localised scleroderma, having a linear, atrophic depression on the frontoparietal scalp.

   Synonym: (abbreviation) ECDS

   • 1962, Harry Maximilian Robinson, Patient presentations of the 12th International Congress of Dermatology:

     The patient is an unusual example of bilateral scleroderma en coup de sabre with distortion of both upper eyelids, and ocular complications.

   • 1980, Neurology, India, Neurological Society of India:

     The clinical picture was suggestive of a combination of scleroderma en coup de sabre and facial hemiatrophy (Parry-Romberg syndrome).
     Distinction between Parry-Romberg syndrome and linear scleroderma with facial atrophy can be quite difficult and it has been postulated that en coup de sabre type may actually be a forme fruste of progressive facial hemiatrophy.

   • 2003, The Journal of Rheumatology:

     Two out of 7 patients with scleroderma en coup de sabre also had morphea elsewhere. These findings strongly favor a close relationship between PFH and scleroderma.

   • 2009, Thomas J.A. Lehman, A Clinician's Guide to Rheumatic Diseases in Children, Oxford University Press, →ISBN:

     Linear scleroderma en coup de sabre is a particular form of linear scleroderma that may not truly be related to the other forms.

   • 2011, Amy S. Paller, Anthony J. Mancini, Hurwitz Clinical Pediatric Dermatology E-Book: A Textbook of Skin Disorders of Childhood and Adolescence, Elsevier Health Sciences, →ISBN, page 520:

     The en coup de sabre variety probably represents a more superficial form of progressive facial hemiatrophy (the Parry–Romberg syndrome), a condition of slowly progressive atrophy of the soft tissue of half of the face with or without associated dermal sclerosis.

en coup de sabre (uncountable)

1. (medicine) A subtype of localised scleroderma that presents with a linear, atrophic depression on the frontoparietal scalp.

   Synonym: (abbreviation) ECDS

   • 1994, Gary M. White, Color atlas of regional dermatology, Mosby Inc, →ISBN:

     A linear, indurated depression running vertically just to one side of the midline is characteristic of en coup de sabre, a variant of morphea.

   • 1996, Richard D. Sontheimer, Thomas T. Provost, Cutaneous Manifestations of Rheumatic Diseases, Lippincott Williams & Wilkins:

     There is a strong association between en coup de sabre and facial hemiatrophy, which often becomes the major clinical problem.

   • 2002, Charles Stephen Foster, Albert T. Vitale, Diagnosis and Treatment of Uveitis, W.B. Saunders Company, →ISBN:

     An area of scleral loss in a patient with en coup de sabre or linear scleroderma involving the face, including eyelids.